International PFAPA syndrome registry: cohort of 214 patients
نویسندگان
چکیده
Address: 1Pediatric Rheumatology of Suisse Romande, Lausanne – Geneva, Switzerland, 2Pediatric Rheumatology, Bordeaux, France, 3Pediatric Rheumatology, Gothenburg, Sweden, 4Pediatric Rheumatology, Haifa, Israel, 5Pediatric Rheumatology, Prag, Czech Republic, 6Pediatric Rheumatology, Kremlin-Bicêtre, France, 7Pediatric Rheumatology, Barcelona, Spain, 8Unit of auto-inflammatory diseases, Montpellier, France, 9Pediatric Rheumatology, Paris, France, 10Pediatric Rheumatology, Lucerne, Switzerland, 11Pediatric Rheumatology, Rome, Italy, 12Pediatric Rheumatology, Lyon, France, 13Pediatric Rheumatology, Leuven, Belgium and 14Pediatric Rheumatology, Genoa, Italy * Corresponding author
منابع مشابه
Periodic Fever, Aphthous Stomatitis, Pharyngitis and Cervical Adenitis (PFAPA) Syndrome in Iranian Children First Report of Iranian Periodic Fever and Autoinflammatory Registry (IPFAIR)
OBJECTIVE The periodic fever, aphthous stomatitis, pharyngitis and cervical adenitis (PFAPA) syndrome is a nonhereditary idiopathic febrile syndrome belonging to the group of autoinflammatory diseases. No longtime sequel was reported in this disease. Early diagnosis can lead physicians to treatment of this disorder with a short course steroid application and provide satisfaction of the patient'...
متن کاملInternational periodic fever, aphthous stomatitis, pharyngitis, cervical adenitis syndrome cohort: description of distinct phenotypes in 301 patients.
OBJECTIVES The aims of this study were to describe the clinical features of periodic fever, aphthous stomatitis, pharyngitis and cervical adenitis (PFAPA) and identify distinct phenotypes in a large cohort of patients from different countries. METHODS We established a web-based multicentre cohort through an international collaboration within the periodic fevers working party of the Pediatric ...
متن کاملPeriodic Fever accompanied by Aphthous stomatitis, Pharyngitis, and cervical Adenitis syndrome (PFAPA syndrome) in adults
BACKGROUND The new syndrome, known as PFAPA, of periodic fever characterized by abrupt onset of fever, malaise, aphthous stomatitis, tonsillitis, pharyngitis and cervical adenopathy has been described only in pediatric patients. It usually begins before the age of 5 years and in most cases resolves spontaneously before age 10. OBJECTIVES To describe a series of adults with PFAPA syndrome. M...
متن کاملTrials Organisation (PRINTO) and the Eurofever/Eurotraps Projects". Treatment of autoinflammatory diseases: results from the Eurofever Registry and a literature review. ANNALS OF THE RHEUMATIC DISEASES
Objective To evaluate the response to treatment of autoinflammatory diseases from an international registry and an up‐to‐date literature review. Methods The response to treatment was studied in a web‐based registry in which clinical information on anonymised patients with autoinflammatory diseases was collected retrospectively as part of the Eurofever initiative. Participating hos...
متن کاملPW03-003 – Altered neutrophil function in PFAPA
Introduction The PFAPA syndrome is a non-mendelian autoinflammatory disease of unknown aetiology characterized by Periodic Fever, Aphthous stomatitis, Pharyngitis, and cervical Adenitis. In typical cases, attacks begin before the age of five and occur every 2-8 weeks, often with striking periodicity. We have previously profiled the blood cells and serum cytokine levels in a cohort study of pati...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
عنوان ژورنال:
دوره 6 شماره
صفحات -
تاریخ انتشار 2008